Multiple destructive changes in the maxillofacial region of the patient with Saethre-Chotzen syndrome (clinical case report)

Abstract

The number of patients with malformations of bone tissue development that apply to the clinics of maxillofacial surgery is not so great, in comparison with other diseases. However, this pathology exists, and the ability to correctly diagnose and apply the necessary treatment tactics is necessary. Of these rare diseases, one should note various forms of dysplastic processes, which are often combined with genetically determined changes.

This article describes the clinical observation of the step-by-step treatment of a patient with Saethre-Chotzen syndrome, with multiple combined destructive changes of the upper and lower jaw. Saethre-Chotzen syndrome is a rare genetic disease in which there are systemic malformations of bone tissue, which entail a disruption of the internal organs and systems. Attention is drawn to the need for an integrated approach to the treatment of dental diseases in patients with this pathology.

Keywords: Saethre-Chotzen syndrome, dysplasia, cyst, cystectomy, curettage.